Advances in basic and clinical research in laminopathies

نویسندگان

  • Luisa Politano
  • Nicola Carboni
  • Agnieszka Madej-Pilarczyk
  • Michael Marchel
  • Gerardo Nigro
  • Anna Fidziaóska
  • Grzegorz Opolski
  • Irena Hausmanowa-Petrusewicz
چکیده

Lamins (LMNA) are the main proteins of the nuclear lamina considered to be the ancestors of all intermediate filament proteins. They form complex protein assemblies with integral proteins of the inner nuclear membrane, transcriptional regulators, histones and chromatin modifiers. During recent years, interest in lamins has greatly increased due to the identification of many distinct heritable human disorders associated with lamin mutations. These disorders, collectively termed laminopathies, range from muscular dystrophies to premature aging. They may affect muscle, fat, bone, nerve and skin tissues. The workshop was addressed to understand lamin organization and its roles in nuclear processes, mutations in lamins affecting cell and tissues functions, the biology of the nucleus and laminopathic disease mechanisms, all aspects important for designing future therapies.

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Laminopathies: many diseases, one gene. Report of the first Italian Meeting Course on Laminopathies

The first Italian Meeting Course on Laminopathies entitled “Laminopathies: many diseases, one gene” was held in Bologna on April 8-9, 2011 and it was attended by 100 participants, including neurologists, dermatologists, cardiologists, biologists, geneticists, and physiotherapists besides patients and families Associations. This meeting was organized by the Institute of Molecular Genetics of the...

متن کامل

Laminopathies and the long strange trip from basic cell biology to therapy.

The main function of the nuclear lamina, an intermediate filament meshwork lying primarily beneath the inner nuclear membrane, is to provide structural scaffolding for the cell nucleus. However, the lamina also serves other functions, such as having a role in chromatin organization, connecting the nucleus to the cytoplasm, gene transcription, and mitosis. In somatic cells, the main protein cons...

متن کامل

ACHIEVEMENTS AND ADVANCES IN DIABETES RESEARCH OVER A QUARTER OF A CENTURY: A REVIEW OF THE AVAILABLE EVIDENCE

Background: Endocrinology and Metabolism Research Institute (EMRI) is one of the largest research institutes in Iran, which has been established to develop research strategies and manage endocrine and metabolic diseases such as diabetes. The purpose of this report is to review and summarize research activities related to diabetes over a quarter of a century at EMRI. Methods: A comprehensive se...

متن کامل

Program evaluation of an integrated basic science medical curriculum in Shiraz Medical School, using CIPP evaluation model

Introduction: In recent years curriculum reform and integrationwas done in many medical schools. The integrated curriculum isa popular concept all over the world. In Shiraz medical school,the reform was initiated by stablishing the horizontal basicscience integration model and Early Clinical Exposure (ECE)for undergraduate medical education. The purpose of this studywas to provide the required ...

متن کامل

Journal of Advances in Medical Education & Professionalism

Medical education is a new discipline whichstarted about 50 years ago. The pioneer of thisdiscipline was George Miller from the Universityof Chicago who suggested most of prominentmedical professionals have little or no knowledge ofpsychology of learning and advocated the validity ofpresent medical education in the world.He hypothesized that while very eminent and welltrained scientific oriente...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

عنوان ژورنال:

دوره 32  شماره 

صفحات  -

تاریخ انتشار 2013